Profile of patient with cystic fibrosis treated in a reference university hospital of Minas Gerais/Brasil

Abstract

Introduction: Advances in the management of cystic fibrosis (CF) allowed a significant increase in life expectancy of fibrocystic individuals. Objective: To characterize the epidemiological and clinical profile of CF patients assisted by the outpatient clinic of a reference university hospital in the treatment of the disease. Methods: A retrospective descriptive study was carried out from January to August 2015. Results: The mean age of the patients in the evaluation period and the mean age at diagnosis were 10.06 ± 6.93 and 1.71 ± 3.28 years, respectively. The majority of the population was female, caucasian, eutrophic, resident outside the reference municipality, had pancreatic insufficiency, bacterial colonization and performed respiratory exercises, as oriented in the outpatient clinic. The mean of the Shwachman-Kulczycki score was 88.63 ± 11.09. Conclusion: This favorable profile shows that a good adherence to the treatment  and understanding about the guidelines offered by the multiprofessional team contributed to the maintenance of good general condition and stabilization of the symptoms.